منابع مشابه
Acquired double-barrel oesophagus in epidermolysis bullosa dystrophica.
An unusual case of epidermolysis bullosa dystrophica with extensive stenosis, high perforation, and dissection of the oesophagus forming a "double-barrel" structure is described. Gastric epithelium found in the upper oesophagus is thought to be of metaplastic origin and caused by repeated minor trauma with repair.
متن کاملDrug-induced cicatricial pemphigoid and acquired epidermolysis bullosa.
A utoimmune diseases probably have a multitude of causes. It is obvious that exogenous agents, particularly drugs, may trigger the development of autoimmune responses leading to bullous eruptions. In the literature several cases of drug-induced (disseminated) bullous pemphigoid (BP) have been reported (see article by Fellner in this issue); however, localized variants of pemphigoid and acquired...
متن کاملEpidemiology of epidermolysis bullosa in the antipodes: the Australasian Epidermolysis Bullosa Registry with a focus on Herlitz junctional epidermolysis bullosa.
OBJECTIVE To present epidemiologic and clinical data from the Australasian Epidermolysis Bullosa (EB) Registry, the first orphan disease registry in Australia. DESIGN Observational study (cross-sectional and longitudinal). SETTING Australian private dermatology practice, inpatient ward, and outpatient clinic. PATIENTS Systematic case finding of patients with EB simplex, junctional EB (JEB...
متن کاملEpidermolysis bullosa acquisita.
Autoimmunity to type-WI collagen is characterized by autoantibodies predominantly of lgG class to the non-collagenous domain of type-WI collagen present in the anchoring fibrils which bind basement membrane lamina densa to the anchoring plaques in the dermis. This results in a sublami.na densa split with a blister formation. Type WI collagen autoim.munity is heterogenous in its clinical spectru...
متن کاملJunctional epidermolysis bullosa.
Epidermolysis bullosa (EB) encompasses a heterogeneous group of genodermatoses, characterized by fragility and blistering of the skin, often associated with extracutaneous manifestations. The level of vesiculation within the skin defines 3 major subtypes of EB: EB simplex, junctional EB, and dystrophic EB. We present the case of a male neonate of 36 weeks of gestation, who was born with a few b...
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ژورنال
عنوان ژورنال: Proceedings of the Royal Society of Medicine
سال: 1929
ISSN: 0035-9157
DOI: 10.1177/003591572902201213